Monomelic amyotrophy: clinical profile and natural history of 279 cases seen over 35 years (1976-2010).
Nalini Atchayaram, Gourie-Devi Mandavilli, Thennarasu Kandavel, +1 more·Amyotrophic lateral sclerosis & frontotemporal degeneration
Our objective was to study the clinical characteristics and natural history of monomelic amyotrophy (MMA). We used a retrospective study of 279 patients diagnosed to have either upper (Hirayama disease) or lower limb MMA. Results showed that brachial MMA (BMMA) occurred in 224 patients (male:female, 9:1). Mean age of o…