Qualitative analysis of factors affecting adherence to the phenylketonuria diet in adolescents.
Sharman Rachael, Mulgrew Kate, Katsikitis Mary·Clinical nurse specialist CNS
PURPOSE/OBJECTIVE: Phenylketonuria (PKU) is an inborn error of metabolism that is primarily treated with a severely restricted, low-protein diet to prevent permanent neurological damage. Despite the recognition of the importance of strict dietary adherence in the prevention of intellectual impairment in individuals wit…